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ICD 10 Diagnosis Codes related to Combined immunodeficiencies (16 entries)

Chapter: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
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D81 - Combined immunodeficiencies
D81.0 - Severe combined immunodeficiency [SCID] with reticular dysgenesis
D81.1 - Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
D81.2 - Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
D81.3 - Adenosine deaminase [ADA] deficiency
D81.4 - Nezelof's syndrome
D81.5 - Purine nucleoside phosphorylase [PNP] deficiency
D81.6 - Major histocompatibility complex class I deficiency
D81.7 - Major histocompatibility complex class II deficiency
D81.8 - Other combined immunodeficiencies
D81.81 - Biotin-dependent carboxylase deficiency
D81.810 - Biotinidase deficiency
D81.818 - Other biotin-dependent carboxylase deficiency
D81.819 - Biotin-dependent carboxylase deficiency, unspecified
D81.89 - Other combined immunodeficiencies
D81.9 - Combined immunodeficiency, unspecified