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277.6 - Other Deficiencies Of Circulating Enzymes


The ICD 9 Code for Other deficiencies of circulating enzymes is listed as 277.6.
Additional information concerning this code and description can be found below including ICD 10 crosswalks / GEMS, and chapter information where available.
ICD 9 CM Field Value
Diagnosis Code: 277.6
Long Description: Other deficiencies of circulating enzymes
Short Description: Defic circul enzyme NEC
Chapter: Endocrine, Nutritional And Metabolic Diseases, And Immunity Disorders
Block: Other Metabolic Disorders And Immunity Disorders (270-279)
Related Descriptions: 6-Pyruvoyl-tetrahydrobiopterin synthase deficiency
Acetyl-CoA: carboxylase deficiency
Acid phosphatase deficiency
Alpha-2-antitrypsin deficiency
Bifunctional peroxisomal enzyme deficiency
Biotinidase deficiency
Clinical manifestation of carnosinase deficiency
Clinical manifestation of enzyme deficiency
Combined deficiency of sialidase AND beta galactosidase
Complex V deficiency
Cytochrome p450 CYP1A2 enzyme deficiency
Cytochrome p450 CYP2C19 enzyme deficiency
Cytochrome p450 CYP2C9 enzyme deficiency
Cytochrome p450 CYP2D6 enzyme deficiency
Cytochrome p450 CYP2E1 enzyme deficiency
Cytochrome p450 CYP3A enzyme deficiency
Cytochrome p450 enzyme deficiency
Deficiency of (R)-20-hydroxysteroid dehydrogenase
Deficiency of (S)-2-hydroxy-acid oxidase
Deficiency of 1,3-beta-glucan synthase
Deficiency of 1,4-alpha-glucan 6alpha-glucosyltransferase
Deficiency of 1,4-alpha-glucan branching enzyme
Deficiency of 2,4-dienoyl-CoA reductase
Deficiency of 2,5-diaminovalerate aminotransferase
Deficiency of 2-hydroxyglutarate dehydrogenase
Deficiency of 2-methylbutyryl-CoA dehydrogenase
Deficiency of 3'-nucleotidase
Deficiency of 3-hydroxyacyl-CoA dehydrogenase
Deficiency of 3-hydroxybutyrate dehydrogenase
Deficiency of 3-hydroxybutyryl-CoA epimerase
Deficiency of 3-hydroxyisobutyrate dehydrogenase
Deficiency of 3-hydroxyisobutyryl CoA hydrolase
Deficiency of 3-mercaptopyruvate sulfurtransferase
Deficiency of 3-oxoacid CoA-transferase
Deficiency of 3-oxoadipate CoA-transferase
Deficiency of 3alpha-hydroxycholanate dehydrogenase
Deficiency of 3alpha-hydroxysteroid dehydrogenase
Deficiency of 4-hydroxy-2-oxoglutarate aldolase
Deficiency of 5'-nucleotidase
Deficiency of 6-phosphofructokinase
Deficiency of A-ase
Deficiency of acetate kinase
Deficiency of acetate-CoA ligase
Deficiency of acetoacetyl-CoA reductase
Deficiency of acetyl-CoA acetyltransferase
Deficiency of acetyl-CoA acylase
Deficiency of acetyl-CoA acyltransferase
Deficiency of acetyl-CoA deacylase
Deficiency of acetyl-CoA hydrolase
Deficiency of acetylcholinesterase
Deficiency of acetylesterase
Deficiency of acetylserotonin methyltransferase
Deficiency of acid-aminoacid ligase
Deficiency of acid-ammonia ligase
Deficiency of aconitate hydratase
Deficiency of acylphosphatase
Deficiency of adenine deaminase
Deficiency of adenine phosphoribosyltransferase
Deficiency of adenosine kinase
Deficiency of adenosine monophosphate deaminase
Deficiency of adenosinetriphosphatase
Deficiency of adenosylhomocysteinase
Deficiency of adenylate kinase
Deficiency of adenylylsulfate kinase
Deficiency of ADP deaminase
Deficiency of alanine aminotransferase
Deficiency of alanine dehydrogenase
Deficiency of alanine-oxo-acid aminotransferase
Deficiency of alanine-tRNA ligase
Deficiency of alcohol sulfotransferase
Deficiency of aldehyde dehydrogenase (NAD^+^)
Deficiency of aldehyde oxidase
Deficiency of aldehyde reductase
Deficiency of aldehyde-lyase
Deficiency of aldonolactonase
Deficiency of aldose 1-epimerase
Deficiency of alkaline phosphatase
Deficiency of alkaline phosphomonoesterase
Deficiency of alkylhalidase
Deficiency of allantoicase
Deficiency of allantoinase
Deficiency of alpha- and beta-trypsin
Deficiency of alpha-1,4-glucan-protein synthase (UDP-forming)
Deficiency of alpha-aminoacylpeptide hydrolase
Deficiency of alpha-amylase
Deficiency of alpha-galactosidase
Deficiency of alpha-glucosidase
Deficiency of amidase
Deficiency of amidinotransferase
Deficiency of amidophosphoribosyltransferase
Deficiency of amine oxidase (copper-containing)
Deficiency of amine oxidase
Deficiency of aminoacyl-histidine dipeptidase
Deficiency of aminoacyltransferase
Deficiency of aminopeptidase
Deficiency of aminotransferase
Deficiency of ammonia-lyase
Deficiency of AMP nucleosidase
Deficiency of amylase
Deficiency of amylo-1,6-glucosidase
Deficiency of arginine deiminase
Deficiency of aromatic-L-amino-acid decarboxylase
Deficiency of aryl sulfotransferase
Deficiency of arylamine acetyltransferase
Deficiency of arylesterase
Deficiency of arylsulfatase
Deficiency of asparagine-oxo-acid aminotransferase
Deficiency of aspartate 4-decarboxylase
Deficiency of aspartate aminotransferase
Deficiency of aspartate carbamoyltransferase
Deficiency of aspartate kinase
Deficiency of aspartic proteinase
Deficiency of ATP pyrophosphatase
Deficiency of azobenzene reductase
Deficiency of benzaldehyde dehydrogenase (NADP^+^)
Deficiency of benzoylcholinesterase
Deficiency of beta-amylase
Deficiency of beta-fructofuranosidase
Deficiency of beta-galactosidase
Deficiency of beta-glucosidase
Deficiency of beta-glucuronidase
Deficiency of beta-ureidopropionase
Deficiency of betaine-aldehyde dehydrogenase
Deficiency of betaine-homocysteine methyltransferase
Deficiency of bisphosphoglycerate mutase
Deficiency of bisphosphoglycerate phosphatase
Deficiency of butyrate-acetoacetate CoA-transferase
Deficiency of butyrylcholine esterase
Deficiency of carbamate kinase
Deficiency of carbon-carbon lyase
Deficiency of carbon-halide lyase
Deficiency of carbon-nitrogen lyase
Deficiency of carbon-oxygen lyase
Deficiency of carbon-sulfur lyase
Deficiency of carbonate dehydratase
Deficiency of carboxy-lyase
Deficiency of carboxylesterase
Deficiency of carboxylic ester hydrolase
Deficiency of carboxypeptidase A
Deficiency of carboxypeptidase B
Deficiency of carnitine acetyltransferase
Deficiency of carnosinase
Deficiency of catalase
Deficiency of catechol oxidase
Deficiency of cathepsin C
Deficiency of cellulase
Deficiency of chlorophyllase
Deficiency of cholate-CoA ligase
Deficiency of cholesterol esterase
Deficiency of cholesterol oxidase
Deficiency of choline acetyltransferase
Deficiency of choline dehydrogenase
Deficiency of choline esterase I
Deficiency of choline esterase II (unspecific)
Deficiency of choline kinase
Deficiency of choline-phosphate cytidylyltransferase
Deficiency of cholinephosphotransferase
Deficiency of cholinesterase
Deficiency of chymosin
Deficiency of chymotrypsin
Deficiency of chymotrypsin A and B
Deficiency of citrate(si)-synthase
Deficiency of coenzyme-A transferase
Deficiency of creatine kinase
Deficiency of cysteamine dioxygenase
Deficiency of cysteine aminotransferase
Deficiency of cysteine carboxypeptidase
Deficiency of cysteine proteinase
Deficiency of cysteinyl-glycine dipeptidase
Deficiency of cystine reductase (NADH)
Deficiency of cytidine deaminase
Deficiency of cytochrome-b>5< reductase
Deficiency of cytochrome-c peroxidase
Deficiency of cytosol aminopeptidase
Deficiency of D-2-hydroxy-acid dehydrogenase
Deficiency of D-amino-acid oxidase
Deficiency of D-aspartate oxidase
Deficiency of D-lactate dehydrogenase
Deficiency of dehydrogenase
Deficiency of dehydrogluconate dehydrogenase
Deficiency of dehydrogluconokinase
Deficiency of deoxyribonuclease I
Deficiency of deoxyribonuclease II
Deficiency of dephospho-CoA kinase
Deficiency of dextranase
Deficiency of dihydrolipoamide acetyltransferase
Deficiency of dihydroorotase
Deficiency of dihydrouracil dehydrogenase (NAD^+^)
Deficiency of diisopropyl-fluorophosphatase
Deficiency of dimethylallyltranstransferase
Deficiency of dioxygenase
Deficiency of dipeptidase
Deficiency of dipeptide hydrolase
Deficiency of dipeptidyl peptidase I
Deficiency of dipeptidyl-amino-peptidase I
Deficiency of dipeptidylpeptide hydrolase
Deficiency of diphosphomevalonate decarboxylase
Deficiency of diphosphoric monoester hydrolase
Deficiency of DNA nucleotidylexotransferase
Deficiency of DNA-directed DNA polymerase
Deficiency of DNA-directed RNA polymerase
Deficiency of endo-1,3(4)-beta-glucanase
Deficiency of endopeptidase
Deficiency of endoribonuclease
Deficiency of enolase
Deficiency of enoyl-CoA hydratase
Deficiency of enteropeptidase
Deficiency of epimerase
Deficiency of erythritol kinase
Deficiency of estradiol 6beta-monooxygenase
Deficiency of ethanolamine-phosphate cytidylyltransferase
Deficiency of ethanolaminephosphotransferase
Deficiency of ether hydrolase
Deficiency of exoribonuclease
Deficiency of ferroxidase
Deficiency of formaldehyde dehydrogenase
Deficiency of formamidase
Deficiency of formate dehydrogenase
Deficiency of formate-tetrahydrofolate ligase
Deficiency of formiminotetrahydrofolate cyclodeaminase
Deficiency of formyltetrahydrofolate deformylase
Deficiency of fructose-bisphosphatase
Deficiency of fructose-bisphosphate aldolase
Deficiency of fumarate hydratase
Deficiency of fumarylacetoacetase
Deficiency of galactonolactone dehydrogenase
Deficiency of galactose dehydrogenase
Deficiency of gentisate l,2-dioxygenase
Deficiency of glucan 1,3-alpha-glucosidase
Deficiency of glucan 1,4-alpha-glucosidase
Deficiency of glucokinase
Deficiency of gluconate 2-dehydrogenase
Deficiency of gluconokinase
Deficiency of gluconolactonase
Deficiency of glucosamine acetyltransferase
Deficiency of glucosamine kinase
Deficiency of glucosamine-6-phosphate isomerase
Deficiency of glucosamine-phosphate acetyltransferase
Deficiency of glucose dehydrogenase
Deficiency of glucose oxidase
Deficiency of glucose-1-phosphatase
Deficiency of glucose-1-phosphate phosphodismutase
Deficiency of glucose-6-phosphate dehydrogenase
Deficiency of glutamate decarboxylase
Deficiency of glutamate dehydrogenase
Deficiency of glutamate-ammonia ligase
Deficiency of glutaminase
Deficiency of glutamine phenylacetyltransferase
Deficiency of glutamine-fructose-6-phosphate aminotransferase (isomerizing)
Deficiency of glutamine-pyruvate aminotransferase
Deficiency of glutarate-CoA ligase
Deficiency of glutathione reductase (NAD(P)H)
Deficiency of glutathione synthase
Deficiency of glutathione thiolesterase
Deficiency of glutathione-homocystine transhydrogenase
Deficiency of glyceraldehyde-3-phosphate dehydrogenase
Deficiency of glycerate kinase
Deficiency of glycerol kinase
Deficiency of glycerol-3-phosphate acyltransferase
Deficiency of glycerophosphatase
Deficiency of glycerophosphocholine phosphodiesterase
Deficiency of glycine acyltransferase
Deficiency of glycine amidinotransferase
Deficiency of glycine formiminotransferase
Deficiency of glycine hydroxymethyltransferase
Deficiency of glycosulfatase
Deficiency of glycosyltransferase
Deficiency of GMP synthase (glutamine-hydrolysing)
Deficiency of guanidinoacetate kinase
Deficiency of guanidinoacetate methyltransferase
Deficiency of guanine deaminase
Deficiency of heparin lyase
Deficiency of hexokinase
Deficiency of hexose oxidase
Deficiency of hexosyltransferase
Deficiency of histidine ammonia-lyase
Deficiency of histidine decarboxylase
Deficiency of histidinol dehydrogenase
Deficiency of homocysteine desulfhydrase
Deficiency of homoserine kinase
Deficiency of hyaluronate lyase
Deficiency of hyaluronoglucosaminidase
Deficiency of hydrogen-sulfide acetyltransferase
Deficiency of hydrolase
Deficiency of hydrolyase
Deficiency of hydroxyacylglutathione hydrolase
Deficiency of hydroxyalkyl-protein kinase
Deficiency of hydroxymethylglutaryl-CoA hydrolase
Deficiency of hydroxymethylglutaryl-CoA lyase
Deficiency of hydroxymethylglutaryl-CoA reductase (NADPH)
Deficiency of hydroxymethylglutaryl-CoA synthase
Deficiency of hypoxanthine phosphoribosyltransferase
Deficiency of imidodipeptidase
Deficiency of iminodipeptidase
Deficiency of IMP cyclohydrolase
Deficiency of inorganic pyrophosphatase
Deficiency of inosinase
Deficiency of inosine monophosphate dehydrogenase
Deficiency of inosine nucleosidase
Deficiency of iodide peroxidase
Deficiency of isocitrate dehydrogenase (NAD^+^)
Deficiency of isocitrate lyase
Deficiency of isoleucine-tRNA ligase
Deficiency of isomerase
Deficiency of isopentenyl-diphosphate delta-isomerase
Deficiency of ketohexokinase
Deficiency of ketotetrose-phosphate aldolase
Deficiency of kynurenine 3-monooxygenase
Deficiency of kynurenine-oxoglutarate aminotransferase
Deficiency of L-amino-acid oxidase
Deficiency of L-arabinose dehydrogenase
Deficiency of L-asparagine amidohydrolase
Deficiency of L-gulonate dehydrogenase
Deficiency of L-lactate dehydrogenase (cytochrome)
Deficiency of L-lactate dehydrogenase
Deficiency of L-prolylglycine dipeptidase
Deficiency of L-serine dehydratase
Deficiency of lactate racemase
Deficiency of lactonase
Deficiency of lactoylglutathione lyase
Deficiency of lecithinase D
Deficiency of leucine aminopeptidase
Deficiency of leucine aminotransferase
Deficiency of leucine-tRNA ligase
Deficiency of lichenase
Deficiency of ligase
Deficiency of lipophosphodiesterase II
Deficiency of long-chain fatty-acyl-CoA hydrolase
Deficiency of long-chain-fatty-acid-CoA ligase
Deficiency of lyase
Deficiency of lysine racemase
Deficiency of lysine-tRNA ligase
Deficiency of lysolecithin acylmutase
Deficiency of lysophospholipase
Deficiency of lysozyme
Deficiency of malate dehydrogenase (decarboxylating)
Deficiency of malate dehydrogenase
Deficiency of malate dehydrogenase (oxaloacetate-decarboxylating)
Deficiency of malate oxidase
Deficiency of maleylacetoacetate isomerase
Deficiency of malonate CoA-transferase
Deficiency of malonyl-CoA decarboxylase
Deficiency of maltose phosphorylase
Deficiency of mannitol dehydrogenase
Deficiency of mannokinase
Deficiency of mannose-6-phosphate isomerase
Deficiency of metallocarboxypeptidase
Deficiency of metalloproteinase
Deficiency of methenyltetrahydrofolate cyclohydrolase
Deficiency of methionine adenosyltransferase
Deficiency of methionine-tRNA ligase
Deficiency of methylaspartate mutase
Deficiency of methylcrotonoyl-CoA carboxylase
Deficiency of methylenetetrahydrofolate dehydrogenase (NADP^+^)
Deficiency of methylglutaconyl-CoA hydratase
Deficiency of methylmalonyl-CoA mutase
Deficiency of methyltransferase
Deficiency of mevaldate reductase
Deficiency of mevalonate kinase
Deficiency of monodehydroascorbate reductase (NADH)
Deficiency of monooxygenase
Deficiency of mutase
Deficiency of myo-inositol oxygenase
Deficiency of N-acetyl-beta-glucosaminidase
Deficiency of N-acetylneuraminate lyase
Deficiency of N-methyl-L-amino-acid oxidase
Deficiency of NAD(P)H dehydrogenase (quinone)
Deficiency of NAD(P)^+^ nucleosidase
Deficiency of NAD(P)^+^ transhydrogenase
Deficiency of NADase
Deficiency of NADH dehydrogenase (ubiquinon)
Deficiency of NADPH-ferrihemoprotein reductase
Deficiency of NAD^+^ kinase
Deficiency of NAD^+^ nucleosidase
Deficiency of NAD^+^ synthase (glutamine-hydrolysing)
Deficiency of NAPH cytochrome-c>2< reductase
Deficiency of nicotinamide methyltransferase
Deficiency of nicotinamide phosphoribosyltransferase
Deficiency of nicotinamide-nucleotide adenylyltransferase
Deficiency of nicotinate dehydrogenase
Deficiency of nicotinate phosphoribosyltransferase
Deficiency of nitrate reductase
Deficiency of non-specific cholinesterase
Deficiency of nucleosidase
Deficiency of nucleoside-diphosphatase
Deficiency of nucleoside-diphosphate kinase
Deficiency of nucleoside-phosphate kinase
Deficiency of nucleotidase
Deficiency of nucleotide pyrophosphatase
Deficiency of nucleotidyltransferase
Deficiency of O-acetylserine (thiol)-lyase
Deficiency of omega peptidase
Deficiency of orotate phosphoribosyltransferase
Deficiency of oxalate CoA-transferase
Deficiency of oxidase
Deficiency of oximinotransferase
Deficiency of oxo-acid-lyase
Deficiency of oxoglutarate dehydrogenase (lipoamide)
Deficiency of oxygenase
Deficiency of palmitoyl-CoA hydrolase
Deficiency of pancreatic elastase
Deficiency of pantetheine kinase
Deficiency of pantetheine-phosphate adenylyltransferase
Deficiency of pantothenoylcysteine decarboxylase
Deficiency of pectin methoxylase
Deficiency of pectin methylesterase
Deficiency of pectinesterase
Deficiency of pentosyltransferase
Deficiency of pepsin A
Deficiency of pepsin B
Deficiency of peptidase a
Deficiency of peptide hydrolase
Deficiency of peptidoglycan endopeptidase
Deficiency of peroxidase
Deficiency of phenylalanine 4-monooxygenase
Deficiency of phenylpyruvate tautomerase
Deficiency of phosphatase
Deficiency of phosphatidate phosphatase
Deficiency of phosphoacetylglucosamine mutase
Deficiency of phosphoadenylate 3'-nucleotidase
Deficiency of phosphoamidase
Deficiency of phosphoglucokinase
Deficiency of phosphogluconate dehydrogenase (decarboxylating)
Deficiency of phosphogluconate dehydrogenase
Deficiency of phosphoglycerate kinase
Deficiency of phosphoglycerate mutase
Deficiency of phosphoketolase
Deficiency of phospholipase A>2<
Deficiency of phospholipase C
Deficiency of phospholipase D
Deficiency of phosphomevalonate kinase
Deficiency of phosphomonoesterase
Deficiency of phosphopantothenate-cysteine ligase
Deficiency of phosphoprotein phosphatase
Deficiency of phosphoribokinase
Deficiency of phosphoribosylamine-glycine ligase
Deficiency of phosphoribosylaminoimidazole carboxylase
Deficiency of phosphoribosylaminoimidazole-succinocarboxamide synthase
Deficiency of phosphoribosylaminoimidazolecarboxamide formyltransferase
Deficiency of phosphoribosylformylglycinamidine cyclo-ligase
Deficiency of phosphoribosylformylglycinamidine synthase
Deficiency of phosphoribosylglycinamide formyltransferase
Deficiency of phosphoric diester hydrolase
Deficiency of phosphoric monoester hydrolase
Deficiency of phosphorus-oxygen lyase
Deficiency of phosphorylase phosphatase
Deficiency of phosphoserine phosphatase
Deficiency of phosphotransferase
Deficiency of plasmin
Deficiency of polygalacturonase
Deficiency of polyribonucleotide nucleotidyltransferase
Deficiency of progesterone 11alpha-monooxygenase
Deficiency of prolidase
Deficiency of prolinase
Deficiency of proline dipeptidase
Deficiency of prolyl dipeptidase
Deficiency of propionyl-CoA carboxylase
Deficiency of protein kinase
Deficiency of protocatechuate 3,4-dioxygenase
Deficiency of pyridoxal kinase
Deficiency of pyridoxamine-phosphate oxidase
Deficiency of pyrophosphotransferase
Deficiency of pyrroline-2-carboxylate reductase
Deficiency of pyrroline-5-carboxylate reductase
Deficiency of pyruvate decarboxylase
Deficiency of quinate dehydrogenase
Deficiency of racemase
Deficiency of reductase
Deficiency of renin
Deficiency of retinal isomerase
Deficiency of retinyl-palmitate esterase
Deficiency of rhamnulokinase
Deficiency of riboflavin kinase
Deficiency of riboflavin mononucleotide adenylyltransferase
Deficiency of ribokinase
Deficiency of ribonuclease
Deficiency of ribose-5-phosphate isomerase
Deficiency of ribose-phosphate pyrophosphokinase
Deficiency of ribosomal cathepsin
Deficiency of ribosomal neutral proteinase
Deficiency of ribosylnicotinamide kinase
Deficiency of ribulokinase
Deficiency of ribulose-phosphate 3-epimerase
Deficiency of sarcosine oxidase
Deficiency of sedoheptulokinase
Deficiency of serine carboxypeptidase
Deficiency of serine proteinase
Deficiency of serine-tRNA ligase
Deficiency of shikimate dehydrogenase
Deficiency of sialidase
Deficiency of squalene monooxygenase
Deficiency of steroid 11-beta-monooxygenase
Deficiency of steroid 17-alpha-monooxygenase
Deficiency of steroid 21-monooxygenase
Deficiency of steroid delta-isomerase
Deficiency of succinate dehydrogenase
Deficiency of succinate-CoA ligase (ADP-forming)
Deficiency of succinate-CoA ligase
Deficiency of succinate-CoA ligase (GDP-forming)
Deficiency of succinyl-CoA hydrolase
Deficiency of sulfatase
Deficiency of sulfate adenylyltransferase (ADP)
Deficiency of sulfinoalanine decarboxylase
Deficiency of sulfite reductase
Deficiency of sulfotransferase
Deficiency of sulfuric ester hydrolase
Deficiency of sulfurtransferase
Deficiency of tannase
Deficiency of thetin-homocysteine methyltransferase
Deficiency of thiamin pyridinylase
Deficiency of thiamin pyrophosphokinase
Deficiency of thioethanolamine acetyltransferase
Deficiency of thioether hydrolase
Deficiency of thiolester hydrolase
Deficiency of thiosulfate sulfurtransferase
Deficiency of threonine aldolase
Deficiency of threonine dehydratase
Deficiency of threonine-tRNA ligase
Deficiency of thymidine phosphorylase
Deficiency of transacylase
Deficiency of transaldolase
Deficiency of transcarbamoylase
Deficiency of transcarboxylase
Deficiency of transferase
Deficiency of transformiminase
Deficiency of transformylase
Deficiency of transhydroxymethylase
Deficiency of transketolase
Deficiency of triacylglycerol lipase
Deficiency of trimetaphosphatase
Deficiency of triokinase
Deficiency of tripeptide aminopeptidase
Deficiency of triphosphoric monoester hydrolase
Deficiency of tropinesterase
Deficiency of true cholinesterase
Deficiency of trypsin
Deficiency of tryptophan 2,3-dioxygenase
Deficiency of tryptophan 5-monooxygenase
Deficiency of tryptophan-tRNA ligase
Deficiency of tyraminase
Deficiency of tyrosine aminotransferase
Deficiency of tyrosine decarboxylase
Deficiency of tyrosine-tRNA ligase
Deficiency of UDPglucose dehydrogenase
Deficiency of unspecific monooxygenase
Deficiency of uracil dehydrogenase
Deficiency of uracil phosphoribosyltransferase
Deficiency of urate oxidase
Deficiency of urease
Deficiency of uridine diphosphate-glucose-hexose-1-phosphate uridylyltransferase
Deficiency of uridine phosphorylase
Deficiency of uronolactonase
Deficiency of UTP-glucose-1-phosphate uridylyltransferase
Deficiency of valine-tRNA ligase
Deficiency of w-amidase
Deficiency of xanthine oxidase
Deficiency of xylan endo-1,3-beta-xylosidase
Deficiency of xylulokinase
Disorder involving deficiency of steryl-sulfatase (EC 3.1.6.2)
Glycerol kinase deficiency - contiguous gene syndrome
Hereditary angioneurotic edema
Hereditary angioneurotic edema with normal C1 esterase inhibitor activity
Metachromatic leukodystrophy due to deficiency of cerebroside sulfatase activator
Muscle L-lactate dehydrogenase deficiency
Pancreatic alpha-amylase deficiency
Phosphoglycerokinase deficiency
Specific enzyme deficiency
Succinate-coenzyme Q reductase deficiency
Ubiquinone dehydrogenase
ICD-10-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD-10-CM Code: D84.1 - Defects in the complement system (approximate)
ICD-9-CM Siblings (same level / similar specificity) of 277.6:
277.1 - Disorders of porphyrin metabolism
277.2 - Other disorders of purine and pyrimidine metabolism
277.4 - Disorders of bilirubin excretion
277.5 - Mucopolysaccharidosis
277.7 - Dysmetabolic syndrome X
277.9 - Unspecified disorder of metabolism