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E88.42 - MERRF syndrome


The ICD 10 Code for MERRF syndrome is listed as E88.42.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: E88.42
Description: MERRF syndrome
  • Myoclonic epilepsy associated with ragged-red fibers
  • Code also myoclonic epilepsy (G40.3-)
Diagnostic Related Groups
(MS-DRG v30.0)
642 - Inborn And Other Disorders Of Metabolism
Chapter Endocrine, nutritional and metabolic diseases (E00-E89)
Block Metabolic disorders (E70-E88)
Parent E88.4 - Mitochondrial metabolism disorders
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 277.87 - Disorders of mitochondrial metabolism (approximate)
ICD-10-CM Siblings (same level / similar specificity) of E88.42:
E88.40 - Mitochondrial metabolism disorder, unspecified
E88.41 - MELAS syndrome
E88.49 - Other mitochondrial metabolism disorders