eMedCodes logo

E88.01 - Alpha-1-antitrypsin deficiency


The ICD 10 Code for Alpha-1-antitrypsin deficiency is listed as E88.01.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: E88.01
Description: Alpha-1-antitrypsin deficiency
  • AAT deficiency
Diagnostic Related Groups
(MS-DRG v30.0)
642 - Inborn And Other Disorders Of Metabolism
Chapter Endocrine, nutritional and metabolic diseases (E00-E89)
Block Metabolic disorders (E70-E88)
Parent E88.0 - Disorders of plasma-protein metabolism, not elsewhere classified
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 273.4 - Alpha-1-antitrypsin deficiency
ICD-10-CM Siblings (same level / similar specificity) of E88.01:
E88.09 - Other disorders of plasma-protein metabolism, not elsewhere classified