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E78.3 - Hyperchylomicronemia


The ICD 10 Code for Hyperchylomicronemia is listed as E78.3.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: E78.3
Description: Hyperchylomicronemia
  • Chylomicron retention disease
  • Fredrickson's hyperlipoproteinemia, type I or V
  • Hyperlipidemia, group D
  • Mixed hyperglyceridemia
Diagnostic Related Groups
(MS-DRG v30.0)
642 - Inborn And Other Disorders Of Metabolism
Chapter Endocrine, nutritional and metabolic diseases (E00-E89)
Block Metabolic disorders (E70-E88)
Parent E78 - Disorders of lipoprotein metabolism and other lipidemias
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 272.3 - Hyperchylomicronemia
ICD-10-CM Siblings (same level / similar specificity) of E78.3:
E78.0 - Pure hypercholesterolemia
E78.1 - Pure hyperglyceridemia
E78.2 - Mixed hyperlipidemia
E78.4 - Other hyperlipidemia
E78.5 - Hyperlipidemia, unspecified
E78.6 - Lipoprotein deficiency
E78.7 - Disorders of bile acid and cholesterol metabolism
E78.8 - Other disorders of lipoprotein metabolism
E78.9 - Disorder of lipoprotein metabolism, unspecified