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E76.22 - Sanfilippo mucopolysaccharidoses


The ICD 10 Code for Sanfilippo mucopolysaccharidoses is listed as E76.22.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: E76.22
Description: Sanfilippo mucopolysaccharidoses
  • Mucopolysaccharidosis, type III (A) (B) (C) (D)
  • Sanfilippo A syndrome
  • Sanfilippo B syndrome
  • Sanfilippo C syndrome
  • Sanfilippo D syndrome
Diagnostic Related Groups
(MS-DRG v30.0)
642 - Inborn And Other Disorders Of Metabolism
Chapter Endocrine, nutritional and metabolic diseases (E00-E89)
Block Metabolic disorders (E70-E88)
Parent E76.2 - Other mucopolysaccharidoses
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 277.5 - Mucopolysaccharidosis (approximate)
ICD-10-CM Siblings (same level / similar specificity) of E76.22:
E76.21 - Morquio mucopolysaccharidoses
E76.29 - Other mucopolysaccharidoses