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E75.4 - Neuronal ceroid lipofuscinosis


The ICD 10 Code for Neuronal ceroid lipofuscinosis is listed as E75.4.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: E75.4
Description: Neuronal ceroid lipofuscinosis
  • Batten disease
  • Bielschowsky-Jansky disease
  • Kufs disease
  • Spielmeyer-Vogt disease
Diagnostic Related Groups
(MS-DRG v30.0)
056 - Degenerative Nervous System Disorders W Mcc
057 - Degenerative Nervous System Disorders W/o Mcc
Chapter Endocrine, nutritional and metabolic diseases (E00-E89)
Block Metabolic disorders (E70-E88)
Parent E75 - Disorders of sphingolipid metabolism and other lipid storage disorders
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 330.1 - Cerebral lipidoses (approximate)
ICD-10-CM Siblings (same level / similar specificity) of E75.4:
E75.0 - GM2 gangliosidosis
E75.1 - Other and unspecified gangliosidosis
E75.2 - Other sphingolipidosis
E75.3 - Sphingolipidosis, unspecified
E75.5 - Other lipid storage disorders
E75.6 - Lipid storage disorder, unspecified