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E71.3 - Disorders of fatty-acid metabolism


The ICD 10 Code for Disorders of fatty-acid metabolism is listed as E71.3.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: E71.3
Description: Disorders of fatty-acid metabolism
  • Excludes1: peroxisomal disorders (E71.5)
  • Refsum's disease (G60.1)
  • Schilder's disease (G37.0)
  • Excludes2: carnitine deficiency due to inborn error of metabolism (E71.42)
Chapter Endocrine, nutritional and metabolic diseases (E00-E89)
Block Metabolic disorders (E70-E88)
Parent E71 - Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
ICD-10-CM Children (deeper level / typically more specific) of E71.3:
E71.30 - Disorder of fatty-acid metabolism, unspecified
E71.31 - Disorders of fatty-acid oxidation
E71.32 - Disorders of ketone metabolism
E71.39 - Other disorders of fatty-acid metabolism
ICD-10-CM Siblings (same level / similar specificity) of E71.3:
E71.0 - Maple-syrup-urine disease
E71.1 - Other disorders of branched-chain amino-acid metabolism
E71.2 - Disorder of branched-chain amino-acid metabolism, unspecified
E71.4 - Disorders of carnitine metabolism
E71.5 - Peroxisomal disorders