eMedCodes logo

E70.0 - Classical phenylketonuria


The ICD 10 Code for Classical phenylketonuria is listed as E70.0.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: E70.0
Description: Classical phenylketonuria
Diagnostic Related Groups
(MS-DRG v30.0)
642 - Inborn And Other Disorders Of Metabolism
Chapter Endocrine, nutritional and metabolic diseases (E00-E89)
Block Metabolic disorders (E70-E88)
Parent E70 - Disorders of aromatic amino-acid metabolism
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 270.1 - Phenylketonuria [PKU] (approximate)
ICD-10-CM Siblings (same level / similar specificity) of E70.0:
E70.1 - Other hyperphenylalaninemias
E70.2 - Disorders of tyrosine metabolism
E70.3 - Albinism
E70.4 - Disorders of histidine metabolism
E70.5 - Disorders of tryptophan metabolism
E70.8 - Other disorders of aromatic amino-acid metabolism
E70.9 - Disorder of aromatic amino-acid metabolism, unspecified