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D80.1 - Nonfamilial hypogammaglobulinemia


The ICD 10 Code for Nonfamilial hypogammaglobulinemia is listed as D80.1.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: D80.1
Description: Nonfamilial hypogammaglobulinemia
  • Agammaglobulinemia with immunoglobulin-bearing B-lymphocytes
  • Common variable agammaglobulinemia [CVAgamma]
  • Hypogammaglobulinemia NOS
Diagnostic Related Groups
(MS-DRG v30.0)
814 - Reticuloendothelial & Immunity Disorders W Mcc
815 - Reticuloendothelial & Immunity Disorders W Cc
816 - Reticuloendothelial & Immunity Disorders W/o Cc/mcc
Chapter Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block Certain disorders involving the immune mechanism (D80-D89)
Parent D80 - Immunodeficiency with predominantly antibody defects
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 279.00 - Hypogammaglobulinemia, unspecified
ICD-10-CM Siblings (same level / similar specificity) of D80.1:
D80.0 - Hereditary hypogammaglobulinemia
D80.2 - Selective deficiency of immunoglobulin A [IgA]
D80.3 - Selective deficiency of immunoglobulin G [IgG] subclasses
D80.4 - Selective deficiency of immunoglobulin M [IgM]
D80.5 - Immunodeficiency with increased immunoglobulin M [IgM]
D80.6 - Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
D80.7 - Transient hypogammaglobulinemia of infancy
D80.8 - Other immunodeficiencies with predominantly antibody defects
D80.9 - Immunodeficiency with predominantly antibody defects, unspecified