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D76.1 - Hemophagocytic lymphohistiocytosis


The ICD 10 Code for Hemophagocytic lymphohistiocytosis is listed as D76.1.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: D76.1
Description: Hemophagocytic lymphohistiocytosis
  • Familial hemophagocytic reticulosis
  • Histiocytoses of mononuclear phagocytes
Diagnostic Related Groups
(MS-DRG v30.0)
814 - Reticuloendothelial & Immunity Disorders W Mcc
815 - Reticuloendothelial & Immunity Disorders W Cc
816 - Reticuloendothelial & Immunity Disorders W/o Cc/mcc
Chapter Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block Other disorders of blood and blood-forming organs (D70-D77)
Parent D76 - Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 288.4 - Hemophagocytic syndromes (approximate)
ICD-10-CM Siblings (same level / similar specificity) of D76.1:
D76.2 - Hemophagocytic syndrome, infection-associated
D76.3 - Other histiocytosis syndromes