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D68.0 - Von Willebrand's disease


The ICD 10 Code for Von Willebrand's disease is listed as D68.0.
Additional information concerning this code and description can be found below including ICD 9 crosswalks / GEMS, chapter information, and DRGs where available.

ICD 10 CM Field Value
Diagnosis Code: D68.0
Description: Von Willebrand's disease
  • Angiohemophilia
  • Factor VIII deficiency with vascular defect
  • Vascular hemophilia
  • Excludes1: capillary fragility (hereditary) (D69.8)
  • factor VIII deficiency NOS (D66)
  • factor VIII deficiency with functional defect (D66)
Diagnostic Related Groups
(MS-DRG v30.0)
813 - Coagulation Disorders
Chapter Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)
Block Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
Parent D68 - Other coagulation defects
ICD-9-CM Diagnosis Codes General Equivalence Mappings (GEMS):
ICD 9 Dx Code: 286.4 - Von Willebrand's disease
ICD-10-CM Siblings (same level / similar specificity) of D68.0:
D68.1 - Hereditary factor XI deficiency
D68.2 - Hereditary deficiency of other clotting factors
D68.3 - Hemorrhagic disorder due to circulating anticoagulants
D68.4 - Acquired coagulation factor deficiency
D68.5 - Primary thrombophilia
D68.6 - Other thrombophilia
D68.8 - Other specified coagulation defects
D68.9 - Coagulation defect, unspecified